Erythromelanosis Follicularis Faciei et Colli
Erythromelanosis follicularis faciei et colli is a rare disorder with well defined, red brown pigmentation and follicular papules on the sides of the face and neck, usually beginning in childhood or adolescence.
It is described mainly in Asian men (Japan, India, China), though cases are reported worldwide. Onset is in the first or second decade, and the course is chronic but may improve in adulthood.
Some cases are familial, but the genetic basis is unknown. It is sometimes seen with keratosis pilaris and atrophic keratosis pilaris of the face.
Pathophysiology.
The cause is unknown. Follicular keratinisation, dilated superficial vessels and increased basal pigment are seen in biopsies. Sun exposure, hormonal influences and an abnormal response to topical substances have been suggested.
